OnlineIMD
Kynurenine-3-hydroxylase deficiency
Type
Disease
External link(s)
IEMbase
Gene
KMO
/ Kynurenine 3-monooxygenase
1q43
OMIM
GnomAD
Ensembl
HGNC
VMH
LOVD
Gene product
Kynurenine 3-monooxygenase
Pathway
Lysine, hydroxylysine, and tryptophan metabolism
Disease group(s)
1.8 Disorders of lysine, hydroxylysine, and tryptophan metabolism